I am very glad to say that a woman's dream come true. In October 2014, it was reported that a 36 years old Swedish woman, who was diagnosed with Rokitansky Syndrome and was undergone womb transplant, gave birth to a healthy baby.
Mayer-Rokitansky-Küster-Hauser Syndrome
Mayer-Rokitansky-Küster-Hauser Syndrome is a disorder that affects female reproductive system. It is a congenital malformation, characterized by a failure of development of mullerian duct, resulting in underdevelopment of uterus and vaginal hypoplasia.
It may be associated with other malformations such as renal agenesis, ectopia of kidneys and cardiac anomalies.
Signs and Symptoms
- Primary Amenorrhea
- Infertility
- Difficulty with sexual intercourse
- History of recurrent urinary tract infection
Management
Goal: To provide the patient with an unscarred vagina
- Perineal dilation
- Vaginal reconstruction by Mclndoe technique with skin graft
- William's vaginoplasty with vulval flap
- Intestinal neovagina uses an isolated segment of bowel
- Uterus transplantation
In conclusion, the risk for transmission of the disease can not be predicted, as the genetics of the MRKH Syndrome is very little known currently.
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